Introduction:

• Long QT Syndrome (LQTS) is a life threatening geneticallyinherited cardiac arrhythmia disorder affecting approximately 1:2500 persons1, often diagnosed in childhood.

• Management of LQTS changes patients’ lifestyles which can affect quality of life (QoL). Patients have restrictions in physical activity, diet, treatment of noncardiac conditions; take daily doses of medicine and/or have implantable cardiac devices (pacemaker/defibrillator).

• General pediatirc cardiac patients show significantly worse QoL in comparison to healthy controls2,3.

• Nearly 1 in 5 with other cardiac disorders reported impaired psychosocial functioning3.

• The effects of implanted cardiac rhythm devices in cardiac patients demonstrated a significant effect on QoL in pediatric patient scores4. • LQTS patients are typically not assessed for psychological symptoms.

• Little research on QoL in pediatric LQTS patients has been conducted to determine if psychosocial interventions are warranted.