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Radiologic features of Hallervorden Spatz Disease
Journal of Pakistan Medical Association
  • K B Asumal, Aga Khan University
  • M Wasay, Aga Khan University
  • S N Ali, Aga Khan University
Publication Date
11-1-2002
Document Type
Report
Disciplines
Abstract

Hallervorden Spatz Disease is a rare familial neurodegenerative disorder, which primarily affects children but also can occur in adults1 . Major clinical features are abnormal involuntary movements and cognitive impairment2 . Diagnosis is based on clinical and radiological features. The radiological features are hypointense signals in globus pallidus and substantia niagra on MR! of brain3 . Occasionally the pallidal hypointense signals surround hyperintense signals, this is known as “tigereye-sign”4 and is postulated to be specific for Hallervorden Spatz Disease. We report two brothers with such MRI findings.

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Citation Information
K B Asumal, M Wasay and S N Ali. "Radiologic features of Hallervorden Spatz Disease" Journal of Pakistan Medical Association Vol. 52 Iss. 11 (2002) p. 528 - 530
Available at: http://works.bepress.com/mohammad_wasay/168/