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Article
Spontaneous left anterior descending coronary artery dissection in a patient with neurofibromatosis
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  • Gregory Giugliano, MD, Baystate Health
  • Prabhdeep Sethi, MD, Baystate Health
Document Type
Article, Peer-reviewed
Publication Date
6-1-2009
Abstract
Neurofibromatosis (NF) is a genetic disorder inherited in an autosomal dominant pattern. Subtypes I and II are the most well recognized, and among these, Type I has associated vasculopathy. Less than 3% of patients have vascular involvement, with the renal artery as the most commonly involved vessel. Dissection and rupture of aneurysms in larger arteries such as the subclavian and the aorta have been previously reported. This is the first reported case of a spontaneous coronary artery dissection in a patient with NF-I. Imperative in the percutaneous treatment of coronary artery dissections is early recognition and proactive decision making. Recognition of a possible association between NF and coronary dissections will further facilitate successful and prompt management of this otherwise rare entity.
Publication ISSN
0278-4297
Citation Information
Giugliano G, Sethi P. Spontaneous left anterior descending coronary artery dissection in a patient with neurofibromatosis J Invasive Cardiol 2009 Jun;21(6):E103-5.