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Article
The VHL/HIF Axis in the Development and Treatment of Pheochromocytoma/Paraganglioma
Frontiers in Endocrinology
  • Song Peng
  • Jun Zhang
  • Xintao Tan
  • Yiqiang Huang
  • Jing Xu
  • Natalie Silk, Philadelphia College of Osteopathic Medicine
  • Dianzheng Zhang, Philadelphia College of Osteopathic Medicine
  • Qiuli Liu
  • Jun Jiang
Document Type
Article
Publication Date
1-1-2020
Abstract

Pheochromocytomas and paragangliomas (PPGLs) are rare neuroendocrine tumors originating from chromaffin cells in the adrenal medulla (PCCs) or extra-adrenal sympathetic or parasympathetic paraganglia (PGLs). About 40% of PPGLs result from germline mutations and therefore they are highly inheritable. Although dysfunction of any one of a panel of more than 20 genes can lead to PPGLs, mutations in genes involved in the VHL/HIF axis including

PubMed ID
33329393
Comments

This article was published in Frontiers in Endocrinology, Volume 11.

The published version is available at https://doi.org/10.3389/fendo.2020.586857.

Copyright © 2020 Peng, Zhang, Tan, Huang, Xu, Silk, Zhang, Liu and Jiang. CC BY 4.0.

Citation Information
Song Peng, Jun Zhang, Xintao Tan, Yiqiang Huang, et al.. "The VHL/HIF Axis in the Development and Treatment of Pheochromocytoma/Paraganglioma" Frontiers in Endocrinology Vol. 11 (2020)
Available at: http://works.bepress.com/dianzheng_zhang/104/