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Biventricular arrhythmogenic cardiomyopathy mimicking cardiac sarcoidosis
JACC: Case Reports
  • Mouna Kodali, Advocate Aurora Health
  • Patrycja Galazka, Advocate Aurora Health
  • Asad Ghafoor, Advocate Aurora Health
  • Atul Bhatia, Advocate Aurora Health
  • Suhail Q Allaqaband, Advocate Aurora Health
Affiliations

Aurora Cardiovascular and Thoracic Services, Aurora Sinai/Aurora St. Luke’s Medical Centers

Scholarly Activity Date
1-4-2024
Abstract

Noninvasive imaging is crucial for diagnosing and managing arrhythmogenic cardiomyopathy. Despite advanced multimodality imaging tools, challenges persist in differentiating it from other arrhythmogenic diseases (eg, cardiac sarcoidosis). We present a case of arrhythmogenic cardiomyopathy with an FLNC variant of uncertain significance exhibiting a phenocopy of cardiac sarcoidosis.

Type
Case Report
PubMed ID
38379651
Citation Information

Kodali M, Galazka P, Ghafoor A, Bhatia A, Allaqaband SQ. Biventricular arrhythmogenic cardiomyopathy mimicking cardiac sarcoidosis. JACC: Case Reports. 2024;29(4):102198. doi:10.1016/j.jaccas.2023.102198